Evaluación de la severidad de la maloclusión en niños con osteogénesis imperfecta

Résumé

The occlusion is the way the dental arches are related to each other. This is characterized by a balance between the craniofacial growth which is in harmony with the growth of the maxilla and the jaw in terms of size, shape and position. Measure and quantify the malocclusion is essencial for a good ortodontic diagnosis but also for epidemiological studies where we can measure the prevalence and the incidence of malocclusion in a certain group of people. Osteogenesis Imperfecta (OI) is a conective tissue disease most commonly involving mutation of the genes that codify type I collagen that affects many organs in the body, especially the skeleton. It is characterized by a reduction inbone mass which means bone fragility. The incidence is 1:15,000 newborns, and it affects all races and genders. For many years the Sillence classification was used to organize the different forms of the disease based on clinical, radiographic and genetic criteria, it divides the disease in four major categories. The OI type I is the mildest form of the disease, the type II is lethal at birth and type III and IV is the most severe group of those that survive at birth...