Osteogénesis imperfectaalteraciones orales y médicas en niños
- Carballido Fernández, Jorge
- Monteserín Matesanz, Marta
- Mourelle Martínez, Mª Rosa
- de Nova García, Joaquín
ISSN: 1697-6398, 1697-641X
Ano de publicación: 2013
Volume: 10
Número: 3
Páxinas: 27-31
Tipo: Artigo
Outras publicacións en: Científica dental: Revista científica de formación continuada
Resumo
Introduction: Osteogenesis imperfecta, also called the brittle bone disease, is a disorder characterised by an alteration in the connective tissues of the entire body, including teething. The objective of the study was to evaluate the presence of fractures and the bones affected by them, the presence of dentinogenesis imperfecta, the treatment of osteogenesis imperfecta and the type of biphosphonate administered. Methods: The clinical histories of 17 patients with osteogenesis imperfecta were evaluated. Results: Of the patients, 81% suffered fractures, 24% were of the femur, 53% of the patients presented dentinogenesis imperfecta, 71% of the patients are treated with biphosphonates and 83% with pamidronate. Conclusions: The majority of the patients have suffered fractures during their life, the dentinogenesis imperfecta occurs frequently in these patients and the majority of them are under treatment with biphosphonates.