Fibrohistiocitoma maligno óseo tras degeneración de enfermedad de Paget Caso clínico y revisión de la literatura

  1. D. CECILIA LOPEZ
  2. E. DELGADO DÍAZ
  3. J. A. ZAFRA JIMENEZ
  4. L. CANDEL GARCIA
  5. R. OLAGUIBEL ALVAREZ-VALDES
Journal:
Revista española de cirugía osteoarticular

ISSN: 0304-5056

Year of publication: 1996

Volume: 31

Issue: 186

Pages: 323-327

Type: Article

More publications in: Revista española de cirugía osteoarticular

Abstract

Malignant fibrous histiocytoma of bone is a rare but highly agressive mesenchimal tumor. It usually arises as a primary tumor but sometimes it can be associated with pre-existing bone abnormalities. Histologically it can be missdiagnosed with other tumors. We report a case of malignant fibrous histiocytoma of bone in the femur in a patient with Paget's disease treated by hip desarticulation. We didn't use chemotherapy because his elderly status. At 18 months follow up, the patient is symptom-free and neither local recurrence nor metastasis have been found. A review of the literature has been carried out.