Hipertensión pulmonar (I). Hipertensión arterial pulmonar

  1. Cadenas Menéndez, S.
  2. Martín Moreiras, J.
  3. Álvarez Vega, P.
  4. González Calle, D.
  5. Oterino Manzanas, A.
  6. Escribano Subias, P.
  7. Sánchez Fernández, P.L.
Revista:
Medicine: Programa de Formación Médica Continuada Acreditado

ISSN: 0304-5412

Año de publicación: 2017

Serie: 12

Número: 45

Páginas: 2655-2673

Tipo: Artículo

DOI: HTTPS://DOI.ORG/10.1016/J.MED.2017.11.003 DIALNET GOOGLE SCHOLAR

Otras publicaciones en: Medicine: Programa de Formación Médica Continuada Acreditado

Resumen

Resumen La hipertensión arterial pulmonar (HAP) es una enfermedad vascular pulmonar, que se define en el cateterismo cardíaco derecho, una vez descartadas las principales causas de hipertensión pulmonar precapilar, especialmente enfermedad respiratoria y enfermedad tromboembólica crónica. El estudio de un paciente con HP se realiza a través de un algoritmo en el que se van descartando, por orden de frecuencia, las causas más comunes de HP, cardíacas y respiratorias. Finalmente, si existe sospecha de HAP, se debe realizar un cateterismo cardíaco derecho diagnóstico, además de solicitar los estudios pertinentes para valorar la presencia de alguna de las condiciones asociadas a este diagnóstico: colagenosis, infección por el VIH, cardiopatía congénita e hipertensión portal. En los últimos años se han producido grandes avances en el manejo de los pacientes con HAP, gracias a la aparición de nuevos fármacos y a su utilización en combinación, mediante una estrategia estructurada y dirigida por objetivos.

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