Síndrome de Sturge Weber: combinación de lesiones angiomatosas coroideas y orbitarias en un paciente

  1. J. Martínez-Gutiérrez 1
  2. R. López-Lancho 1
  3. E. Pérez-Blázquez 1
  1. 1 Hospital Universitario 12 de Octubre
    info

    Hospital Universitario 12 de Octubre

    Madrid, España

    ROR https://ror.org/00qyh5r35

Journal:
Archivos de la Sociedad Española de Oftalmologia

ISSN: 0365-6691

Year of publication: 2008

Volume: 83

Issue: 7

Pages: 429-432

Type: Article

DOI: 10.4321/S0365-66912008000700007 DIALNET GOOGLE SCHOLAR lock_openOpen access editor

More publications in: Archivos de la Sociedad Española de Oftalmologia

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Abstract

Case report: We present the case of a 34-year-old man with Sturge-Weber syndrome, who presented to the emergency room with left ocular pain and left chronic exophthalmos. He suffered an acute glaucoma secondary to pupillary block consequent upon an anterior lens subluxation. Orbital contrast Magnetic Resonance Imaging (MRI) was performed and he underwent intracapsular lens extraction. Discussion: The MRI showed T2 enhanced lesions in the left meninges, choroid, and orbit, compatible with cavernous hemangiomas, as well as a dilated superior ophthalmic vein. Intraocular pressure after cataract surgery was 10 mm Hg, and visual acuity was less than 20/200