Enfermedad de Castleman unicéntricaa propósito de un caso

  1. Mikel Rojo Abecia 1
  2. Adelino Pérez Morera 1
  3. David Roldan Cortés 1
  4. Alicia Ruiz de la Hermosa 1
  5. Nefeli Yagüe Rigopoulou 1
  6. Laura Román García de León 1
  7. Gloria Paseiro Crespo 1
  1. 1 Hospital Universitario Infanta Leonor. Madrid.
Zeitschrift:
Cirugía Andaluza

ISSN: 2695-3811,  1130-3212

Datum der Publikation: 2021

Ausgabe: 32

Nummer: 1

Seiten: 70-73

Art: Artikel

DOI: 10.37351/2021321.14 DIALNET GOOGLE SCHOLAR lock_openDialnet editor

Andere Publikationen in: Cirugía Andaluza

Zusammenfassung

Castleman disease was first described in 1956 and is a group of lymphoproliferative disorders that have a common histological pattern. The disease is mainly divided into unicentric or multicentric. Multicentric affects multiple nodal regions. It is frequently associated with HHV-8 in immunodeficient patients, however it can be idiopathic. These patients usually have systemic symptoms. Unicentric Castleman disease affects a single ganglionic region and is usually asymptomatic. It is more common in young, female patients. If symptoms are present, they are usually related to the mass effect caused by the affected nodes. If the disease is resectable, complete removal is curative in most patients. In unresectable cases, other therapies can be used, both systemic, based on immunosuppressants, and local, especially embolization and radiotherapy. We present the case of a 24-year-old female patient studied for pain in her left upper extremity. Complementary tests showed a retropectoral adenopathic conglomerate with no affectation at other levels. The anatomopathological study after surgical resection showed findings compatible with Castleman disease.

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Fuente de los datos: Dialnet